Case Report

Primary Immunodeficiency with Severe Multi-Organ Immune Dysregulation

Table 2

Autoantibodies.

Antibody (units)ResultsReference Range

ANAnegativenegative
DsDNA (IU/mL)1.1<70.1
Rheumatoid factor (IU/mL)<9.90–22
Thyroglobulin (ng/mL)00
Anti-TPO antibody (IU/mL)567.20–5
Glutamic acid decarboxylase antibody (IU/mL)>250<5