Case Report
The Natural History of X-Linked Lymphoproliferative Disease (XLP1): Lessons from a Long-Term Survivor
Table 1
Clinical immunology profile at age 43.
| | Immunoglobulin | Levels | (Normal range) | Immune subsets | Total number (103/uL) | (Normal range) |
| | IgE | <2 | (≤114 kU/L) | Absolute lymphocytes | 1330 | 4500–11000 | | IgG | 1244 | (694–1618 mg/dL) | CD3 + T cells | 1250 | 798–2594 | | IgM | 6 | (48–271 mg/dL) | CD19+ B cells | 40 | 63–461 | | IgA | <5 | (81–463 mg/dL) | CD3-CD16+ CD56+ NK cells | 39 | 89–472 |
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The patient had a therapeutic IgG level but low IgM and IgA levels. Flow cytometry also showed normal T cell counts but low B and NK cell counts.
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