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Case Reports in Medicine
Volume 2012, Article ID 397508, 3 pages
Case Report

Congenital Cystic Adenomatoid Malformation: Is There a Need for Pregnancy Termination?

2nd Department of Obstetrics and Gynecology, University of Athens, Aretaieion Hospital, Athens, Greece

Received 4 April 2011; Revised 3 January 2012; Accepted 6 January 2012

Academic Editor: André Mégarbané

Copyright © 2012 C. Iavazzo et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


Aim. Congenital cystic adenomatoid lung malformation is a rare unilateral dysplasia of the lung. Three pathologic types are described in the literature: type I with cysts >2 cm, type II with cysts <1 cm, and type III with microcysts. The aim of this paper is to present a case of a fetus with congenital cystic adenomatoid lung malformation and discuss the necessity for pregnancy termination according to its prognosis and future mortality. Case. A 36-year-old pregnant woman (para: 1, gravida: 1) presented in our department for anatomy ultrasound screening at 2 0 + 1 weeks of gestation. The ultrasound detected a cystic adenomatoid right lung malformation measuring 1 . 4 5 × 1 . 6 7  cm which caused mediastinal shift of the heart and the lung to the left side. Other findings were cysts of the choroid plexus and echogenic intracardiac foci. The parents after genetic counseling decided pregnancy termination. The pregnant received cabergoline for ablactation. Conclusion. Congenital cystic adenomatoid lung malformation has different prognosis according to the type (69% in type I, 0% in types II and III). Fetal hydrops, cardiac and skeletal anomalies, Potter's syndrome, and gastrointestinal atresia are common cofindings. Genetic counseling is necessary, and pregnancy termination is proposed to the cases with poor prognosis.