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Case Reports in Medicine
Volume 2013, Article ID 404710, 4 pages
Case Report

Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease

1Department of Nephrology, Cumhuriyet University Medical School, 58140 Sivas, Turkey
2Department of Radiology, Cumhuriyet University Medical School, 58140 Sivas, Turkey

Received 2 February 2013; Revised 8 May 2013; Accepted 20 May 2013

Academic Editor: Michael S. Firstenberg

Copyright © 2013 Ayşe Şeker Koçkara et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease and is responsible for 8–10% of patients with end-stage renal failure. The major extrarenal complications of ADPKD are cardiovascular abnormalities. Interrupted aortic arch (IAA) is a lethal congenital cardiac abnormality seen with a frequency of 3/1000000 births and is defined as a segment of the arcus aorta being atresic. In the literature, there are no any reports showing that polycystic kidney disease and interrupted aortic arch occur together. In this study, we present a rare case in which the patient has polycystic kidney disease and IAA together and discuss whether IAA is a complication of ADPKD.