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Author | Patient | Etiology | Principal symptoms | MRI findings | Outcome |
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Flanagan et al. [5] (2013) | 41 M | Unknown, patient with Crohn’s disease | Headache and ataxia and cerebellar signs | T2 signal abnormalities, pial enhancement and cerebellar enlargement | Alive |
Rizek et al. [6] (2013) | 63 F | Salmonella typhimurium (blood culture) | Meningeal signs, appendicular ataxia | Diffuse cerebellar hyperintense signal on T2 sequence | Alive with residual dysarthria and dysmetria |
Ishikawa et al. [7] | 25 F | Influenza A (H3N2) | Dysarthria, slurred speech, limb and truncal ataxia | High signal intensity in the cerebellar cortex on T2-weighted MRI | Alive with partial neurological recovery |
Sugiyama et al. [8] (2000) | 35 F | Unknown | Fever, headache, stiff neck, coma | Diffuse cerebellar cortical, T2 high signal, pontine lesion | Alive, complete recovery |
Ravi and Rozen [9] (2000) | 22 F | Unknown | Ataxia, fever, headache, stiff neck | Diffuse cerebellar swelling, hydrocephalus, leptomeningeal enhancements | Alive with improvement in symptoms |
Bakshi et al. [10] (1998) | 21 M | Unknown | Vomiting, headache | Diffuse cerebellar swelling, herniation of the tonsil, leptomeningeal enhancement | Alive with minimal residual neurological deficits at 1 year |
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