Recoverable, Record-High Lactic Acidosis in a Patient with Glycogen Storage Disease Type 1: A Mixed Type A and Type B Lactate Disorder

Figure 1

Changes in plasma pH and levels of lactate, bicarbonate, sodium, and creatinine during the hospitalization course. The black rectangle and arrow in the middle graph symbolize the period of bicarbonate infusion and the timing of initiation of mechanical ventilation, respectively. The horizontal line represents convenience sodium level of 140 meq/L.