Case Report

Undifferentiated Pleomorphic Sarcoma of Pancreas: A Case Report and Review of the Literature for the Last Updates

Table 1

Cases of primary UPS of the pancreas in English-language literature.

Authors (ref. no.)YearAgeSexHistologic typeLocationTreatmentFollow-up (months)

Margueles et al. [12]197622FMyxoidHeadPancreaticoduodenectomy17, NED
Ishiguchi [41]198644MPleomorphicBody-tailLeft pancreatectomy, splenectomy15, NED
Hasegawa et al. [42]198744MGiant cellBody-tailLeft pancreatectomy, splenectomy7, NED
Garvey et al. [43]198977MStoriform-pleomorphicUncinate lobeEnucleation48, NED
Pascal et al. [44]198939MStoriform-pleomorphicHeadPancreaticoduodenectomy0, DOC
Suster et al. [45]198971MGiant cellHeadPancreaticoduodenectomyNF
Allen et al. [46]199046MStoriform-pleomorphicBody-tail, local invasion80% pancreatectomy, splenectomy, subtotal gastrectomy5, DOD
Filippini et al. [47]199250FMyxoidBody-tailLeft pancreatectomy, splenectomyNF
Tsujimura et al. [48]199243FStoriform-pleomorphicTailPancreatectomy, splenectomy5, NED
Ben [49]199372MStoriform-pleomorphicBody-tailLeft pancreatectomy, splenectomy12, DOD
Balén [50]199337MPleomorphicBody-tailExtended left pancreatectomy7, DOD
Haba et al. [51]199670MStoriform-pleomorphicHeadPancreaticoduodenectomy22, NED
Bastian et al. [13]199967MStoriform-pleomorphicBodyLeft pancreatectomy, splenectomy, transverse colectomy, subtotal gastrectomy34, NED
Liu et al. [5]199927FMyxoidBody-tailLeft pancreatectomy, splenectomy6, NED
Mai et al. [52]200271FGiant cellHeadPancreaticoduodenectomy24, DOD
Darvishian et al. [53]200274MStoriform-pleomorphicHeadPancreaticoduodenectomy4, NED
Akatsu et al. [16]200567MStoriform-pleomorphicBody-tailLeft pancreatectomy, splenectomy, transverse colectomy, total gastrectomy35, NED
Yu et al. [54]200867MStoriform-pleomorphicHeadPancreaticoduodenectomy11, DOD
Jarry et al. [6]201045MStoriform-pleomorphicHeadMultidisciplinary treatment11, NED
Gupta et al. [55]201252MMyxoidBody-tailDistal pancreatectomy, splenectomy2, NED
Current case201672FPleomorphicHead and neckPancreaticoduodenectomy22, NED

M: male; F: female; NF: no follow-up; NED: no evidence of disease; DOD: dead of disease; DOC: dead of perioperative complications.