| Etiologic factors | ā |
| Drugs | Methysergide and other ergot alkaloids, and less commonly, beta blockers, methyldopa, hydralazine, analgesics, etanercept, infliximab | Malignancy | Lymphoma, sarcoma, carcinoid, metastatic disease from primary cancers [e.g. gastrointestinal, breast, lung, genitourinary tract, thyroid]) | Proliferative/infiltrative diseases | Erdheim-Chester disease, other histiocytosis, IgG4-related diseases | Infections | Mycobacterium tuberculosis, histoplasmosis, actinomycosis | Others | Radiation, asbestos exposure, trauma, idiopathic | Clinical manifestations | ā |
| Constitutional symptoms (as a result of underlying disease or consequences of any complications above) | Mild fevers, fatigue, sleepiness, anorexia, hypertension | Circulatory system | Aorta and its branches: Limb ischemia, claudication, testicular pain | Inferior vena cava: Lower extremity deep venous thrombosis/phlebitis, lower extremity edema, varicocele | Gastrointestinal system | Pancreas: Pancreatitis (may be associated with underlying etiology of RPF, i.e. IgG4-related disease) | Intestines (duodenum, ascending and descending colong): Abdominal pain (typically back, nonspecific to lower abdomen), abdominal distension, nausea, weight loss | Urinary tract | Adrenals: Fatigue, malaise | Kidneys, ureters: Oliguria, anuria, kidney failure | Lymphatic system | Lumbar lymph nodes: Lower extremity edema, testicular hydrocele |
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