Case Report

Acute Kidney Failure in a Young African American Male

Table 1

Etiologic factors and clinical manifestations of retroperitoneal fibrosis.

Etiologic factorsā€‰

DrugsMethysergide and other ergot alkaloids, and less commonly, beta blockers, methyldopa, hydralazine, analgesics, etanercept, infliximab
MalignancyLymphoma, sarcoma, carcinoid, metastatic disease from primary cancers [e.g. gastrointestinal, breast, lung, genitourinary tract, thyroid])
Proliferative/infiltrative diseasesErdheim-Chester disease, other histiocytosis, IgG4-related diseases
InfectionsMycobacterium tuberculosis, histoplasmosis, actinomycosis
OthersRadiation, asbestos exposure, trauma, idiopathic
Clinical manifestationsā€‰

Constitutional symptoms (as a result of underlying disease or consequences of any complications above)Mild fevers, fatigue, sleepiness, anorexia, hypertension
Circulatory systemAorta and its branches: Limb ischemia, claudication, testicular pain
Inferior vena cava: Lower extremity deep venous thrombosis/phlebitis, lower extremity edema, varicocele
Gastrointestinal systemPancreas: Pancreatitis (may be associated with underlying etiology of RPF, i.e. IgG4-related disease)
Intestines (duodenum, ascending and descending colong): Abdominal pain (typically back, nonspecific to lower abdomen), abdominal distension, nausea, weight loss
Urinary tractAdrenals: Fatigue, malaise
Kidneys, ureters: Oliguria, anuria, kidney failure
Lymphatic systemLumbar lymph nodes: Lower extremity edema, testicular hydrocele