Case Report

Brain Herniation in Neurofibromatosis with Dysplasia of Occipital Bone and Posterior Skull Base

Table 1

Previously reported cases of occipital meningoencephalocele in NF1.

AuthorAge/sexCasesPresentationManagement

Nakasu et al. (1981) [4]42 yr/M1Occipital scalp neurofibroma and underlying bone defectExcision of scalp tumor with duraplasty and cranioplasty

Renshaw et al. (2003) [5] 54 yr/F1Massive plexiform neurofibroma extending from the left occipital region to shoulder area with large left occipital bone dysplasia and extensive cerebellar meningoencephaloceleResection of the neurofibroma and advancement and rotational skin
flaps

Bodhey and Gupta (2006) [3]28 yr/M1Occipital encephalocele with malignant transformation of overlying scalp neurofibromaBiopsy of the scalp tumour

Dadlani et al. (2013) [1]17 yr/M2Occipital meningoencephalocele with scalp neurofibromaDuraplasty and cranioplasty
14 yr/MOccipital meningoencephalocele with scalp neurofibromaSubtotal excision of tumour with duraplasty

NF1: neurofibromatosis 1; M: male; F: female.