Case Report

Adult Primary Spinal Epidural Extraosseous Ewing’s Sarcoma: A Case Report and Review of the Literature

Table 1

Cases of adult primary spinal epidural EES/PNET tumors in the literature.

AuthorYearAge (years)/sex (M or F)Location/diagnosisTreatmentFollow-up (months)OutcomeCD99t(11:22)Country

Angervall and Enzinger [11]197520/MT2–T5/EESSTR/RT/CT12DODNANASweden
Angervall and Enzinger [11]197518/FL5/EESGTR/RT/CT6DODNANASweden
Scheithauer and Egbert [29]197818/ML1/EESGTR/RT/CT16NEDNANAUSA
Scheithauer and Egbert [29]197827/FT4–T6/EESSTR/RT/CT132NEDNANA USA
Mahoney et al. [30]197823/MS1/EESBiopsy/RT/CT12DODNANA USA
Fink and Meriwether [31]197919/ML2-L3/EESSTR/RT/CT12NEDNANA USA
N’Golet et al. [32]198229/MT1–T3/EESGTR/RT/CT6NEDNANAFrance
N’Golet et al. [32]198247/FL4/EESGTR/RT/CT4DODNANAFrance
Sharma et al. [33]198618/MT10/EESSTR/RT/CT42DODNANAIndia
Liu et al. [34]198726/FL5-S1/PNETSTR/RT6NEDNANATaiwan
Christie et al. [35]199736/FL2-L3/EESSTR/RT96DODNANAAustralia
Dorfmüller et al. [3]199918/ML3-L4/PNETGTR/RT/CT23NED++Austria
Kennedy et al. [36]200024/MC1–C5/EESSTR/RT/CT13NEDNANAIreland
Shin et al. [37]200138/MC5-C6/EESSTR/CT17NED+NASouth Korea
Shin et al. [37]200122/FC7-T1/EESSTR/CT48NED+NASouth Korea
Morandi et al. [38]200122/FT4-T5/EESGTR/RT/CT66NED+NAFrance
Morandi et al. [38]200125/FL1-S2/EESSTR/CT7DOD+NAFrance
Mukhopadhyay et al. [15]200129/FC3–C5/EESSTR/RT/CT30NED+NAIndia
Mukhopadhyay et al. [15]200118/MT8-T9/EESSTR/RT/CT18NED+NAIndia
Mukhopadhyay et al. [15]200122/ML5-S1/EESBiopsy/RT/CT15NED+NAIndia
Mukhopadhyay et al. [15]200131/ML3-L4/EESSTR/RT/CT32NED+NAIndia
Gandhi et al. [39]200333/MT5–T10/EESGTR/RT/CT3NED+NACanada
Weber et al. [40]200426/ML1-L2/PNETGTR/RT/CT16NED+NASwitzerland
Koudelova et al. [41]200628/FL1-L2/PNETSTR/RT/CT24NEDNANACzech Republic
Isefuku et al. [5]200620/ML5-S1/EESSTR/CT15DOD++Japan
Ozturk et al. [8]200718/MC6-T1/EESGTR/CT13NED+NATurkey
Lakhdar et al. [16]200824/FC6-C7/EESGTR/CT/RTNANANANAMorocco
Bozkurt et al. [42]200728/MC3–C5/EESGTR/RT/CT18NED+NATurkey
Feng et al. [43]200824/MT8–T10/PNETGTR/RT14NEDNANAChina
Musahl et al. [44]200827/MS1-S2/PNETGTR/RT/CT24NEDNANA USA
Theeler et al. [9]200928/FT6/NSGTR/CT2NED++ USA
Kiatsoontorn et al. [45]200925/MT7/PNETGTR/RT/CT6NED+NAJapan
Jingyu et al. [19]200958y/MT4/PNETGTR Only25NED+NAChina
Duan et al. [4]201126/FT4–T7/PNETSTR/RT/CT3NED+NAChina
Duan et al. [4]201134/MT12/PNETSTR Only1NED+NAChina
Yasuda et al. [20]201137/FT8-T9/EESSTR/RT/CT22DOD++Japan
Bostelmann et al. [46]201129/MC7/EESSTR/RT/CT6DOD+NAGermany
Saeedinia et al. [7]201244/FS1–S3/NSGTR/RT9NED+NAIran
Zhu et al. [21]201246/MC3–C6/EESSTR/RT/CT12DOD+NAChina
Zhu et al. [21]201227/MC1–C4/EESGTR/RT/CT10NED+NAChina
Zhu et al. [21]201227/MC7/EESGTR/RT/CT24NED+NAChina
Zhu et al. [21]201224y/MC5/EESSTR/RT/CT7DOD+NAChina
Kazanci et al. [12]201534/FT4–T6/EESGTR/RT/CT18NED+NATurkey
Kazanci et al. [12]201565/FT7-T8/EESGTR/RT/CT14NED+NATurkey
García-Moreno et al. [47]201545/FC6-T3/EESSTR/RT/CT8NED++Spain
Present case201540/MT10–T12/EESGTR/RT/CT12NEDNA+ USA

M: male. F: female. EES: extraskeletal Ewing’s sarcoma. PNET: peripheral neuroectodermal tumor. GTR: gross total resection. STR: subtotal (partial) resection. RT: radiotherapy. CT: chemotherapy. NED: no evidence of disease. DOD: dead of disease. NS: not specified.
Country: the country where the cases were reported and studied.