Successful Treatment of Incomplete Susac Syndrome with Simultaneous Corticosteroids and Plasmapheresis Followed by Rituximab

Figure 1

Sagittal views at the level of the corpus callosum during active susac syndrome. (a) T1-weighted. Note. The 6-7 mm T1 hypodensity in the body of the corpus callosum was consistent with a “snowball” lesion (demarcated by an arrow), and T1 linear hypodensity sparing the calloseptal surface of the corpus callosum was consistent with a linear “spoke” or “icicle” lesion (demarcated by an arrow head). (b) Sagittal T2/FLAIR-weighted imaging with gadolinium contrast. Note. The increased T2/FLAIR signal and contrast enhancement in the “snowball” lesion (demarcated by an arrow) were consistent with active susac syndrome.

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