Kaposiform Hemangioendothelioma of the GI Tract: An Exception to Occam’s Principle in an Adult with SBO

Figure 2

Kaposiform hemangioendothelioma histology. (a) The tumor demonstrates clusters of small capillary-sized vessels containing red blood cells, similar to capillary hemangioma. (b) Adjacent to these vascular nodules are scattered ectatic, irregularly shaped vascular channels (asterisks) with a lymphangioma-like morphology. (c) Interspersed throughout the tumor are more cellular regions composed of spindle cells reminiscent of Kaposi sarcoma but without significant cytologic atypia, mitotic activity, or necrosis. (d) The tumor is punctuated by glomeruloid structures, present as rounded nodules of dense vascular tissue associated with red blood cell fragments, hyaline droplets, and finely granular hemosiderin.

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