Peripheral Medulloepithelioma: A Rare Entity to Know

Table 1

Review of literature for peripheral medulloepithelioma cases [3–15].

Reference	Age	Gender	Site	Stage	Metastasis	Therapy	Outcome
Kleinman et al. [11]	20 yr	F	Ovary	I	No	Complete surgery, CT	NED, 108 mo
Kleinman et al.	32 yr	F	Ovary	I	No	Complete surgery, CT	NED, 36 mo
Kleinman et al.	13 yr	F	Ovary	III	No	Complete surgery	DOD, 20 mo
Kleinman et al.	23 yr	F	Ovary	III	No	Complete surgery, CT, RT	DOD, 2 mo
Figarella-Branger et al. [16]	17 yr	F	Pelvis	IV	Lung	Surgery on primitive tumor	DOD, 8 mo
Bruggers et al. [5]	Birth	F	Pelvis	III	No	Partial resection, CT	NED, 50 mo
Donner and Teshima [12]	12 yr	F	Pelvis	III	No	CT	NED, 36 mo
Nakamura et al. [8]	6 mo	M	Pelvis (sciatic nerve)	III	No	Complete surgery	NED, 84 mo
De Pasquale et al. [3]	3 yr	F	Retroperitoneal mass	III	No	Surgery, CT, autograft, RT	NED, 6 mo, then replase
Pillai et al. [10]	3 yr	F	Pelvis	I	No	Complete surgery, CT, RT	NED, 5 mo
Seemayer et al. [7]	5 yr	F	Presacral	—	No	Surgery, RT, CT (after metastasis)	Liver metastases after 2 mo, died 8 mo after diagnosis
Somjee et al. [17]	3 yr	M	Presacral	IV	Liver and lung metastases	CT	On treatment (8 mo)
Tran et al. [18]	5 yr	F	Sacrococcygeal	—	No	Surgery, RT	Recurrence 6 yr after diagnosis, liver metastasis
Lee et al. [19]	Birth	M	Sacrococcygeal	—	—	Surgery, CT	DOD, cerebral metastasis
Honnart et al. [4]	2 yr	F	Presacral	—	No	CT, surgery, rapamycin maintenance	NED 5 yr
Our case	3 yr	F	Presacral	IV	Liver	Partial surgery, CT	Alive

Legend: F: female; M: male; yr: years; mo: months; CT: chemotherapy; RT: radiotherapy; NED: nonevidence of disease; DOD: died of disease.