Fundoscopic Changes in Maroteaux-Lamy Syndrome

Figure 3

(a) Retinographies after penetrating keratoplasty. Multiple areas of orange patches are observed on retinography (arrows). (b) Infrared imaging of the fundus. (c) Enhanced depth imaging optical coherence tomography—the orange patches observed in the retinographies correspond to areas in which deposits of intermediate reflectivity can been seen at the scleral level (white arrows). These lesions are associated with marked choroidal thinning.

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