Bilateral Multiple Focal Choroidal Excavations in a Patient with Paroxysmal Nocturnal Hemoglobinuria (PNH)

Figure 2

EDI-OCT scan of posterior pole of right eye (OD) and left eye (OS). OD1: Multiple focal choroidal excavations were showed in one horizontal scan. The outer nuclear layers (ONLs) conformed to retinal pigment epithelium (RPE) alterations within the excavation. And the RPE layer followed the contour of the choroidal excavation. There is no RPE detachment and no separation between the photoreceptor and the RPE. One area (arrow) of outer nuclear layers (ONLs) beside the excavation became hyperreflective with a density similar to that of the outer plexiform layer (OPL). OD2: Choriocapillaris in the site of excavation (Arrow) is thinner with adjacent large blood vessels changes comparing to the surrounding choroid. OS1: Multiple FCE without involving the fovea. OS2: Similar hyperreflective ONLs revealed in the left eye beside of the FCE lesion (arrow).

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