Macular Changes in a Mucopolysaccharidosis Type I Patient with Earlier Systemic Therapies

Figure 3

Fundus infrared imaging revealed hyperreflective ring centred in the fovea and hyporeflective areas in temporal parafoveal regions in both eyes (a, b). En face SD-OCT images at the level of the outer retina revealed two hyperreflective rings corresponding to the disruption of the ellipsoid zone (c, e) and ELM (d, f). SD-OCT: spectral domain optical coherence tomography; ELM: external limiting membrane.

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