Peripapillary Pachychoroid Syndrome (PPS): Diagnosing and Treating a Rare Entity

Figure 2

A few months later, there was deterioration in the LE: FA of the RE (a) and LE (b) was noncontributory, while ICGA (c and d) showed hyperfluorescence in 4 foci during the late phase of the exam in the LE corresponding to areas of choroidal hyperpermeability (white arrows, (d)). EDI-OCT revealed increased choroidal thickness [max thickness: 431 μm in the RE (e) and 554 μm in the LE (f)], with pachyvessels () located mostly nasally to the fovea and IRF/SRF accumulation in the fovea of the LE (f). OCT images of RE (g) and LE (h) after PDT treatment in LE, showing resolution of CME and SRF in LE. CME observed in the LE 6 months later (i), and fluid absorption after treatment with dexamethasone drops in the LE (j).

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