Successful Treatment of Atlantoaxial Subluxation in an Adolescent Patient with BrachytelephalangicChondrodysplasia Punctata

Figure 2

(a, b) Preoperative anterior-posterior and lateral plain radiographs of the cervical spine revealing multiple dysplastic vertebral bodies (white arrowheads). (c, d) Preoperative lateral plain radiographs of the cervical spine clearly demonstrating unstable atlantoaxial subluxation. (e) An anterior-posterior plain radiograph of the right hand revealing typical shortening of the distal phalanges (brachytelephalangy) of the thumb and middle and ring fingers. (f) Preoperative sagittal reconstructed computed tomography showing the segmented os odontoideum (white arrow). (g) Preoperative sagittal T2-weighted magnetic resonance (MR) images showing a severely compressed spinal cord at the C1/2 level with signs of myelomalacia inside the cord. A low-intensity retroodontoid mass is evident on the T2-weighted MR images. (h) Preoperative axial T2-weighted MR image at the C1/2 level revealing a severely compressed spinal cord. The white dotted lines in (g) indicate the level of (h).

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