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Case Reports in Otolaryngology
Volume 2014, Article ID 703017, 6 pages
http://dx.doi.org/10.1155/2014/703017
Case Report

Chronologic Presentation of a Severe Case of Progressive Hemifacial Atrophy (Parry-Romberg Syndrome) with the Loss of an Eye

Department of Otolaryngology Head & Neck Surgery, Turgut Özal University Hospital, Faculty of Medicine, Turgut Özal University, Alparslan Turkes Caddesi No. 57, 06510 Ankara, Turkey

Received 18 August 2014; Accepted 30 October 2014; Published 18 November 2014

Academic Editor: Harukazu Hiraumi

Copyright © 2014 Mesut Kaya et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Progressive hemifacial atrophy, also known as Parry-Romberg syndrome, is a slowly advancing degenerative disease that mostly affects the cutaneous, subcutaneous fatty tissue, muscle tissue, and bone structures on one side of the face. We describe the chronological progression of this very rare syndrome from early childhood until adulthood in a patient who developed severe atrophy and lost one eye. We also discuss the aetiology and pathophysiology of this syndrome.