Longitudinal Neuropsychological Profile in a Patient with Triple A Syndrome

Table 1

Longitudinal cognitive and neuropsychological assessment.

Examined skill	T0	T1
	At admission	After one year
Cognitive level
WPPSI-III—Wechsler preschool and primary scale of intelligence	TIQ^a: 88; VIQ^b: 98; PIQ^c: 85	TIQ: 91; VIQ: 96; PIQ: 91
Adaptive level
VABS—Vineland Adaptive Behavior Scales:
Communication	a.e.^d 3, 7 years	a.e. 5, 4 years
Daily living skills	a.e. 2, 11 years	a.e. 4, 1 years
Socialization	a.e. 3, 1 years	a.e. 4, 5 years
Motor skills	a.e. 3, 1 years	a.e. 4, 4 years
Visual-Motor Integration
DVMI—Developmental Test of Visual-Motor Integration:
Visual-Motor Integration	Rs^e: 6; Ss^f: 67; a.e. 3, 6 years; 𝑃^g: 1°	Rs: 6; Ss: 62; a.e. 3, 6 years; 𝑃: 1°
Visual-Motor Integration Visual Test	Rs: 13; Ss: 95; a.e. 5, 1 years; 𝑃: 37°	Rs: 13; Ss: 88; a.e. 5, 1 years; 𝑃: 21°
Visual-Motor Integration Motor Test	Rs: 8; Ss: 73; a.e. 3, 5 years; 𝑃: 4°	Rs: 10; Ss: 78; a.e. 4, 1 years; 𝑃: 7°
Attention
Bells Test:
Selective visual attention	<1,9 SD^h	<0,9 SD
Sustained visual attention	<2,3 SD	<0,9 SD
Memory
BVN—Battery for the assessment of neuropsychology for; developmental age
Verbal short-term memory:
Direct	Span: 3; <0,5 SD	Span: 3; <1,3 SD
Reverse	Not evaluable	Not evaluable
PROMEA—Memory and learning tasks for developmental age
Nonword Repetition	Rs: 32; 𝑃: 75°	Rs: 31; 𝑃: 50°
Planning
Tower of London	Not evaluable	Rs: 14; 𝑃: <5°
Motor skills
MABC—Movement Assessment Battery for Children:
Manual dexterity	Rs: 9,5; 𝑃: 5°	Rs: 11; 𝑃: <5°
Ball skills	Rs: 0; 𝑃: >15°	Rs: 6; 𝑃: <5°
Static and dynamic balance	Rs: 12,5; 𝑃: <5°	Rs: 13,5; 𝑃: <5°

 ^aTotal Intelligence Quotient.
^bVerbal Intelligence Quotient.
^cPerformance Intelligence Quotient.
^dAge-equivalent score.
^eRaw score.
^fStandard score.
^gPercentile.
^hStandard deviation.