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Case Reports in Pediatrics
Volume 2013, Article ID 764216, 2 pages
http://dx.doi.org/10.1155/2013/764216
Case Report

Congenital Pulmonary Alveolar Proteinosis

1Pediatrics Department, University of Monastir, Faculty of Medicine, Monastir 5000, Tunisia
2ORL Department, University of Monastir, Faculty of Medicine, Monastir 5000, Tunisia

Received 20 March 2013; Accepted 10 April 2013

Academic Editors: D. J. Licht, G. V. Massey, and I. Riaño Galán

Copyright © 2013 Saber Hammami et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Pulmonary alveolar proteinosis (PAP) is a rare syndrome characterized by pulmonary surfactant accumulation within the alveolar spaces. It occurs with a reported prevalence of 0.1 per 100,000 individuals. Two clinically different pediatric types have been defined as congenital PAP which is fatal and a late-onset PAP which is similar to the adult form and less severe. The clinical course of PAP is variable, ranging from spontaneous remission to respiratory failure. Whole-lung lavage is the current standard treatment for PAP patients. We report a new congenital case of PAP.