Congenital Portosystemic Shunt: Our Experience

Table 1

Clinical manifestations associated with congenital portosystemic shunt [9–15].

Hepatic	Nodular lesions, focal nodular hyperplasia, hepatocellular adenoma, hepatocellular carcinoma, hepatic sarcoma, and newborn cholestasis
Neurological	Behavioral disorders, irritability, dyslexia, lethargy, EEG abnormalities, extrapyramidal signs, and epilepsy
Pulmonary	Dyspnea caused by pulmonary hypertension
Metabolic	Hyperammonemia, hypoglycemia, hyperinsulinaemia, and hypergalactosemia, without evidence of a deficiency of galactokinase or epimerase [1]
Others	IUGR, membranoproliferative glomerulonephritis with proteinuria and IgA stores, coagulation disorders, congestive heart failure, hyperandrogenism, pancreatitis, and autoimmune disorders