A Patient with MSUD: Acute Management with Sodium Phenylacetate/Sodium Benzoate and Sodium Phenylbutyrate

Figure 1

Hemodialysis and Na phenylacetate/benzoate and phenylbutyrate treatment during attack management. 0–28 hrs: Continious venovenous dialysis (through femoral vein) 28. hr: Cloggling of hemodialysis catheter, 32–66. hrs: Na phenylacetate/benzoate, 66. hrs+: Na phenylbutyrate (Pheburane® 483 mg/gr, granulated).