Severe Hepatopulmonary Syndrome in a Child with Caroli Syndrome
Table 1
Hepatopulmonary Syndrome diagnostic criteria.
Variable
Criterion
Oxygenation impairment
Partial pressure of oxygen < 80 mmHg or Alveolar-arterial oxygen gradient ≥ 15 on room air
Pulmonary vascular dilation
Presence of contrast in the left side of the heart after three cardiac cycles on a contrast echocardiography OR abnormal uptake in the brain (>6%) with a Technetium-99 macroaggregate albumin study
Liver disease
Portal hypertension with or without cirrhosis
Level of severity
A-a oxygen ≥ 15 plus
Mild
A partial pressure of oxygen ≥ 80 mmHg
Moderate
A partial pressure of oxygen ≥ 60 mmHg to <80 mmHg
Severe
A partial pressure of oxygen ≥ 50 mmHg to <60 mmHg
