| Onset | Laboratory findings |
| At 3-month old | | Complete blood count (CBC) | Hb 8.2 g/dl, WBC 17,700/mm3 (P 35%, L 60%, monocyte 5%), platelets 521,000/mm3 | Coagulation studies | PT 63.8 sec (N 11–14), INR 5.23 aPTT 69.5 sec (N 23–31), TT 10.6 sec (N 8.7–11.1) | Factor assay (% activity) | FII 5.50% (N 70–140), FVII 10.90% (N 70–140) FIX 7.10% (N 50–200), FX 4.70% (N 50–200) FV 121% (N 70–130), FVIII 148.1% (N 50–200) | Liver function test | AST 55 U/L, ALT 15 U/L, albumin 4.2 g/dL, total birilubin 0.6 mg/dL, direct birilubin 0.3 mg/dL | Fat-soluble vitamins level | Vitamin A 0.87 µmol/L (N 0.8–2.9), vitamin E 14.70 µmol/L (N 8–43), vitamin D (25-OH) 7.51 ng/mL (N 30–100) | At 1-year old | | Complete blood count (CBC) | Hb 7.8 g/dl, WBC 16,200/mm3 (P 92%, L 6%, monocyte 2%), platelets 427,000/mm3 | Coagulation studies | PT 11 sec (N 11–14), INR 1.1 aPTT 26 sec (N 23–31), TT 10 sec (N 8.7–11.1) | Liver function test | AST 45 U/L, ALT 17 U/L, albumin 2.5 g/dL, total birilubin 0.6 mg/dL, direct birilubin 0.3 mg/dL | Immunological studies | IgG 1,236 mg/dL (N 700–1,000), IgM 161 mg/dL (N 40–230), IgA 102 mg/dL (N 70–400) | Ascitic fluid parameter | Straw color, serum ascites albumin gradient (SAAG) 0.5 g/dL, WBC 1,600/mm3 with 100% mononuclear cell adenosine deaminase (ADA) 83 U/L (N 0–33) |
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