Case Sex Age at initial presentation Initial presenting symptom Side Histopathology Outcome Reference 1 M ≤2 y Mass R RE and smooth muscle Surgical excision and resolution Pul and Pul [17 ] 2 M 10 y Mass R RE and lymphoid aggregates Surgical excision and resolution Das et al. [18 ] 3 M ≤2 y Asymptomatic L Not documented Surgical excision and resolution Fraga et al. [10 ] 4 M 2 y Asymptomatic R Not documented Surgical excision and resolution Fraga et al. [10 ] 5 M ≤2 y Asymptomatic L Not documented Surgical excision and resolution Fraga et al. [10 ] 6 M 4 y Mass L RE, goblet cells, smooth muscle, and mucous glands Surgical excision and resolution Yu et al. [19 ] 7 M 46 y Growing mass L RE, sebaceous glands, squamous epithelium, and malignant melanoma Surgical excision, metastasis, and death Tanita et al. [16 ] 8 M ≤2 y Growing mass R RE Surgical excision and resolution Tresser et al. [20 ] 9 M ≤2 y Growing mass L RE, goblet cells, and smooth muscle Surgical excision and resolution Jona [13 ] 10 M 4 y Mass R RE alternating with stratified squamous epithelium, goblet cells, sebaceous glands, and smooth muscle Incision and drainage, subsequent surgical excision , and resolution van der Putte and Toonstra [21 ] 11 F 8 y Asymptomatic RE, goblet cells, and mucous glands Surgical excision and resolution Manconi et al. [22 ] 12 F ≤2 y Draining sinus L RE alternating with stratified squamous epithelium, and mucous glands Surgical excision and resolution Ozel et al. [23 ] 13 M 3 y Draining sinus R RE, stratified squamous epithelium, and lymphoid aggregates Surgical excision and resolution Kundal et al. [24 ] 14 M 3 y Mass L RE Surgical excision and resolution Al-Balushi et al. [11 ] 15 F 5 y Draining sinus L RE and lymphoid aggregates Surgical excision and resolution Farag et al. [12 ] 16 M ≤2 y Abscess R RE, smooth muscle, squamous epithelium, and sebaceous glands Surgical excision and resolution Nakamura et al. [14 ] 17 F 4 y Draining sinus L RE, smooth muscle, and seromucous glands Surgical excision and resolution Blanchard et al. [25 ] 18 M 3 y Abscess L RE Surgical excision and resolution Zhu et al. [9 ] 19 M ≤2 y Draining sinus L RE, squamous epithelium, goblet cells, smooth muscle, and seromucous glands Surgical excision and resolution Sun et al. [15 ] 20 F 5 y Recurrent cellulitis L RE, smooth muscle, mucous glands, and lymphoid aggregates Surgical excision and resolution Current case
