Carglumic Acid Contributes to a Favorable Clinical Course in a Case of Severe Propionic Acidemia

Table 1

Venous blood gas analysis at the time of discharge and at 1, 3, 6, and 12 months after discharge.

	At the time of discharge	1 month	3 months	6 months	12 months
PH	7.35	7.39	7.40	7.36	7.43
BE (mmol/L)	−2.1	−2.7	−5.1	−0.9	−3.3
(mmol/L)	23.4	22.0	19.0	23.8	20.2
NH3 (μmol/L)	25	41	33	36	59