Case Report
Functional Adrenocortical Adenoma in a Child with Beckwith–Wiedemann Syndrome
Table 4
BWS clinical diagnosis criteria.
| Cardinal features (2) points | Suggestive features (1) points |
| Macroglossia Omphalocele | Large birth weight Facial nevus simplex | Lateralized overgrowth Hyperinsulinism | Polyhydramnios and/or placentomegaly | Multifocal/bilateral Wilms tumor or nephroblastomatosis pathogenic findings | Ear creases/pits Umbilical hernia and/or diastasis recti | | Organomegaly | Embryonal tumors | Transient hyperglycemia |
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