Case Report

Functional Adrenocortical Adenoma in a Child with Beckwith–Wiedemann Syndrome

Table 4

BWS clinical diagnosis criteria.

Cardinal features
(2) points
Suggestive features
(1) points

Macroglossia
Omphalocele
Large birth weight
Facial nevus simplex
Lateralized overgrowth
Hyperinsulinism
Polyhydramnios and/or placentomegaly
Multifocal/bilateral Wilms tumor or nephroblastomatosis pathogenic findingsEar creases/pits
Umbilical hernia and/or diastasis recti
Organomegaly
Embryonal tumors
Transient hyperglycemia