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Clinical history | Crohn’s disease | Both | Behçet’s disease |
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Demographics | More common in Northern Europe, Northern America, United Kingdom. Female > male | | Asian and Mediterranean populations. Male > female |
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Genetic and laboratory markers | NOD2/CARD15, ASCA, ANCA | | HLA-B51 |
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Ophthalmologic | Mostly insidious onset. Bilateral anterior uveitis, dry eyes, blepharitis, and episcleritis | Uveitis | More recurrent and sight-threatening. Pan-uveitis or posterior uveitis with necrotizing retinal vasculitis |
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Oral | | Oral aphthous ulcers | |
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Cardiovascular | | Thrombotic events | Superficial thrombophlebitis, venous thrombosis, arterial aneurysm. Pulmonary artery thrombosis |
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Gastrointestinal | On endoscopy, discontinuous longitudinal ulcers (≥4 to 5 cm), cobblestone appearance, and/or small aphthous ulcerations are arranged in a longitudinal fashion. Noncaseating granulomas, cryptic architectural abnormalities, and discontinuous inflammation. Anal strictures, fistula, and abscess formation | Gastrointestinal symptoms | On endoscopy, single or few (≤5), large (>1 cm), discrete, and round or oval-shaped ulcerations in the ileocecal area. Other forms include neutrophilic phlebitis and ischemia damage (vasculitis) |
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Hepatobiliary | Primary sclerosing cholangitis | | Budd-Chiari syndrome |
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Genitourinary | | | Genital ulcers with scar, epididymitis/orchitis |
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Dermatological | Pyoderma gangrenous, sweet’s syndrome, neutrophilic dermatosis | Erythema nodosum | Pathergy, pseudofolliculitis |
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Musculoskeletal | | Peripheral arthritis, sacroiliitis, spondyloarthropathy | |
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Neurological | | | Neuro-Behçet |
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