Case Report

Kawasaki Disease: Unusual Presentation with Retropharyngeal Involvement

Table 1

Criteria for the diagnosis of Kawasaki disease

Fever for more than five days (four days if treatment with IVIG eradicates fever) plus at least four of the following clinical signs not explained by another disease process

(1) Bilateral conjunctival injection
(2) Changes in the oropharyngeal mucous membranes (including >1 of the following symptoms: injected and/or fissured lips, strawberry tongue, injected pharynx)
(3) Changes in the peripheral extremities, including erythema of the hands and feet (acute phase) or periungual desquamation (convalescent phase)
(4) Polymorphous rash, primarily truncal; nonvesicular
(5) Cervical lymphadenopathy: anterior cervical lymph node at least >1.5 cm in diameter

Modified from Robert P. Sundel; Kawasaki disease, Rheum Dis Clin North Am 41 (2015) 63–73.