Table of Contents Author Guidelines Submit a Manuscript
Case Reports in Pulmonology
Volume 2012, Article ID 371490, 3 pages
Case Report

A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis

1Department of Internal Medicine, Geisinger Medical Center, 100 North Academy Avenue, Danville, PA 17822, USA
2Division of Pulmonary and Critical Care, Geisinger Medical Center, 100 North Academy Avenue, Danville, PA 17822, USA

Received 23 September 2012; Accepted 30 October 2012

Academic Editors: H. Niwa, M. Takao, and N. Yoshimura

Copyright © 2012 Ghulam Rehman Mohyuddin et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


A 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right upper lobe bronchus and right mainstem bronchus and secondary atelectatic changes. Biopsy was consistent with a diagnosis of lymphomatoid granulomatosis Grade 3. She responded well clinically and radiologically to therapy. Lymphomatoid granulomatosis is a rare EBV-associated disorder which is considered a lymphoproliferative disease. The most common radiographic feature is multiple lung nodules. An isolated hilar mass is an exceptionally rare presentation of this rare disease.