Undiagnosed Chronic Granulomatous Disease, Burkholderia cepacia complex Pneumonia, and Acquired Hemophagocytic Lymphohistiocytosis: A Deadly Association

Table 3

Chronic granulomatous patients with Burkholderia cepacia complex infection and acquired hemophagocytic lymphohistiocytosis.

Sex	Age	Mutation	Site of infection	Outcome	Reference
M	36 months	X-linked	Abdomen	Survived	[11]
F	19 years	p22-phox	Vagina	Survived	[12]
M	17 months	NS	Spleen	Survived	[13]
M	40 months	X-linked	Lung	Deceased	[14]
M	21 years	p47-phox	Lung	Deceased	Present case

NS: non specified.