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Case Reports in Radiology
Volume 2014, Article ID 202160, 4 pages
Case Report

Klippel-Trénaunay Syndrome with Intracranial Arteriovenous Malformation: A Rare Presentation

1Department of Radiology and Imaging Sciences, Emory University Hospital, Atlanta, GA, USA
2Emory Clinical Cardiovascular Research Institute, Atlanta, GA, USA

Received 22 August 2013; Accepted 12 November 2013; Published 6 February 2014

Academic Editors: D. P. Link and K. Tokunaga

Copyright © 2014 Mahniya F. Sadiq et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.


Klippel-Trénaunay syndrome (KTS) is a rare vascular congenital anomaly affecting less than 200,000 people in the United States. Vascular malformations associated with KTS tend to affect slow flow systems: venous, capillary, and lymphatic systems. The nature of the syndrome leads to a higher risk for the development of arteriovenous malformations. Our case presentation describes a patient with KTS and an associated rare presentation of intraventricular arteriovenous malformation (AVM).