Neuroimaging Features of San Luis Valley Syndrome

Figure 3

Axial T2-weighted fast spin echo image (repetition time msec/echo time msec, 6083/108) demonstrating irregular cerebellar fissuration/foliation consistent with dysplasia (large arrows), enlarged inner ear vestibules representing dysplasia (small arrows), and malformation of the medulla oblongata with underdevelopment of the median sulcus and absent preolivary sulci (arrowhead). The vermis is not present on this transaxial section as it should be, consistent with vermian hypoplasia.