Case Report

Postcardiotomy Mechanical Circulatory Support in Two Infants with Williams’ Syndrome

Table 1

Cases summary.

Case  1Case  2

Age (months)8.513
GenderMaleFemale
Weight 6.7 kg9 kg
Height 71 cm70 cm
Primary diagnosisSupravalvular aortic stenosis, Williams’ syndromeSupravalvular aortic stenosis, pulmonary artery stenosis, Williams-Beuren syndrome
CPB time226 min159 min
Ischaemic time61 min54 min
ECMO support70 hrs44 hrs
APPT (for ACT 140–180)48.9* (32.3–>110)35.2* (31.4–89.4)
ComplicationsHaemorrhage and reexplorationPneumothorax
ICU stay9 days30 days
Total stay16 days39 days

Median value.