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| Group | Associated anomalies | Inheritance |
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| 1 | Scalp ACC without multiple anomalies | Cleft lip and palate, tracheoesophageal fistula, patent ductus arteriosus, omphalocele, mental retardation, polycystic kidneys | Autosomal dominant or sporadic |
| 2 | Scalp ACC with limb abnormalities | Limbs reduced, syndactyly, clubfoot, encephalocele, nail dystrophy or absence, persistent cutis marmorata | Autosomal dominant |
| 3 | Scalp ACC with skin/organoid nevi | Epidermal nevi, organoid nevi, corneal opacities, scleral dermoids, eyelid colobomas, mental retardation, seizures | Sporadic |
| 4 | ACC overlying embryologic malformations | Meningomyelocele, spinal dysraphia, cranial stenosis, leptomeningeal angiomatosis, gastroschisis, congenital midline porencephaly, ectopia of ear, omphalocele | Depends upon underlying condition |
| 5 | ACC with fetus papyraceus or placental infarcts | Single umbilical artery spastic developmental delay, spastic paralysis, clubbed hands and feet, amniotic bands | Sporadic |
| 6 | ACC associated with epidermolysis bullosa | Blistering of skin and/or mucous membranes, deformed nails, pyloric or duodenal atresia, abnormal ears and nose, ureteral stenosis, renal anomalies, amniotic bands | Depends upon type of epidermolysis bullosa |
| 7 | ACC localized to extremities without blistering | None | Autosomal dominant or recessive |
| 8 | ACC caused by teratogens | Imperforate anus (methimazole), other signs of intrauterine infection with varicella or herpes simplex | Not inherited |
| 9 | ACC associated with congenital syndromes | Trisomy 13, 4p-syndrome, ectodermal dysplasia, focal dermal hypoplasia, amniotic band disruption complex, XY gonadal dysgenesis, Johanson-Blizzard syndrome | Depends upon syndrome |
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