Maple Syrup Urine Disease in a Central Indiana Hereford Herd

Table 1

Branched-chain ketoacid concentrations.

Animals	KIV (nmol/g)	KIC (nmol/g)	KMV (nmol/g)
MSUD; Suspect calf	24.92	>362	24.25
3 “Healthy Calves”	1.97	10.92	0.63
Increase in MSUD calf from healthy calves	12.6X	>33X	38.4X

Ketoacid concentrations in the liver of the Hereford calf with maple syrup urine disease versus the average of three “healthy” age-matched but not breed-matched control calves are summarized. KIV: ketoisovaleric, KIC: ketoisocaproic, and KMV: keto-β-methylvaleric acids, respectively.