Poorer Prognosis of Idiopathic Pleuroparenchymal Fibroelastosis Compared with Idiopathic Pulmonary Fibrosis in Advanced Stage
Table 1
The baseline characteristics of IPPFE and IPF patients.
IPPFE
IPF
value
()
()
Sex M/F
9/20
54/13
<0.01
Age (years)
69 ± 7.3
69 ± 7.8
0.81
Smoker/nonsmoker
11/18
56/11
<0.01
Number of pack-years
10.2 ± 20.0
34.7 ± 27.0
<0.01
History of pneumothorax
3 (10%)
1 (1.4%)
0.08
Family history of IPs
3 (10%)
10 (14.9%)
0.40
BMI (kg/m2)
20.1 ± 3.25
24.1 ± 2.97
<0.01
Thoracic dimensions
APDT/TDT (%)
59.9 ± 6.0
65.4 ± 5.2
<0.01
Symptoms
Cough
13 (45%)
20 (30%)
0.16
Dyspnea on exertion
7 (24%)
13 (19%)
0.60
Clubbed finger
6 (21%)
16 (24%)
0.73
Fine crackles
25 (86%)
65 (97%)
0.07
First medical examination
Symptomatic
21 (72%)
32 (48%)
0.03
Mass screening
8 (28%)
35 (52%)
Data presented as the mean ± SD or numbers. IP = interstitial pneumonia; BMI = body mass index; APDT = anteroposterior diameter of the thorax; TDT = transverse diameter of the thorax.