Poorer Prognosis of Idiopathic Pleuroparenchymal Fibroelastosis Compared with Idiopathic Pulmonary Fibrosis in Advanced Stage

Table 5

Annual changes in the pulmonary function parameters.

	IPPFE ()	IPF ()	value
Observation period (years)	1.01 ± 0.19	1.03 ± 0.24	0.59
ΔFVC (L)	–0.28 ± 0.27	–0.11 ± 0.26	0.02
ΔTLC (L)	–0.32 ± 0.26	–0.06 ± 0.39	0.01
ΔRV (L)	–0.04 ± 0.18	–0.07 ± 0.56	0.83
ΔDLco (ml/min/mmHg)	–0.70 ± 1.95	–0.45 ± 1.60	0.87

Data presented as the mean ± SD. Changes in the pulmonary function parameters as assessed at the 1-year follow-up appointment. FVC = forced vital capacity; TLC = total lung capacity; RV = residual volume; DLco = diffusing capacity of the lung for carbon monoxide.