Hypertension, Chronic Kidney Disease, and Renal Pathology in a Child with Hermansky-Pudlak Syndrome

Figure 1

(a) Perihilar segmental sclerosis (PAS, original magnification 20x). (b) Diffuse tubulopathy: variably size tubular profiles, hypertrophic tubular epithelial cells, cytoplasmic vacuolization, and coarse fuchsinophilic cytoplasmic accumulations (trichrome, original magnification 20x). (c) Diffuse tubulopathy: tubular epithelial cell cytoplasmic irregular waxy brown-yellow ceroid-lipofuscin—like pigment accumulations (black arrow) (PAS, original magnification 40x).

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