Cochlear Implantation in Patients with Neurofibromatosis Type 2 and Patients with Vestibular Schwannoma in the Only Hearing Ear

Table 2

Case reports on cochlear implantation and vestibular schwannoma resection regardless of the approach or timing between surgeries.

Author

Patients no.

Age

Approach

Radiation

Time to implantation (m)

Cause HL

Followup (m)

Cochlear implant PTA dB

Speech tests

Telephone

Daily use

EPT after VS resection (m)

Hoffman et al. [12] 1992

1

30

RS

No

4

NF2

12

NA

SRT 53 dB SPL, SDT 43 dB SPL. MAC open set scores: spondees 40%, NU-6 word score 32%, NU-6 phoneme 53%, CID 72%.

Yes

NA

EPS 2 m +

Arriaga and Marks [10] 1995

1

65

TL

No

S

OT,VS

10

25

NA

NA

Yes

NA

Hulka et al. [31] 1995

1

31

RS

No

2

NF2

3

35

NA

NA

Yes

EPS 1.5 m +

Tono et al. [32] 1996

1

48

MF

No

15

NF2

17

NA

Tests with lipreading: MR 60%, WR 70%, SR 81%. Tests without lip reading: MR 24%, WR 62%, SR 43%.

Yes

NA

EPS 1 m +

Temple et al. [33] 1999

1

15

MF

No

9

NF2

12

NA

SRos 100%, 2WPR 70%, 3-4WPR 60%.

NA

NA

EPS 1.5 m +

Graham et al. [34] 1999

1

34

RS

No

84

NF2

10

NA

CUNY with lip reading 97%, BKB 34%, ESR 63%.

NA

Yes

EPS 84 m +

Ahsan et al. [35] 2003

1

53

TL

No

S

NF2

NA

NA

NA

NA

NA

NA

Nölle et al. [36] 2003

1

16

RS

No

24

NF2

24

NA

SRos: 88%

NA

NA

EPS +

TL: translabyrinthine; NA: nonavailable; MF: middle fossa; RS: retrosigmoid; S: simultaneous; NF2: neurofibromatosis type 2; VS: vestibular schwannoma; SRT: speech reception threshold; SDT: speech detection threshold; MAC: minimal auditory capabilities; NU: Northwestern University; CID: Central Institute for the Deaf sentences of everyday speech; MR: monosyllables recognition; WR: word recognition; SR: sentence recognition; EPT: electrical promontory test; EPS: Electrical promontory stimulation; CNAP: compound action potential; SRos: sentence recognition open set; 2WPR: 2 word phrases recognition; 3-4WPR: three-to-four word phrases recognition; CUNY: City University of New York sentences in noise; BKB: BKB sentences in quiet without lip reading; ESR: environmental sound recognition. Bold letters patients who initially had negative promontory stimulation.