International Journal of Rheumatology / 2010 / Article / Tab 2

Research Article

Characteristics of Interstitial Fibrosis and Inflammatory Cell Infiltration in Right Ventricles of Systemic Sclerosis-Associated Pulmonary Arterial Hypertension

Table 2

Characteristics of SScPAH patients.

Antibody- profileCause of deathSSc disease duration Survival after PAH diagnosis (yr)Medication at time of death

1 AnticentromereRV failure40,5prostacyclin
2 LcSScAnticentromereRV failure120,75prostacyclin
3 LcSScAnticentromereRV failure10,08prostacyclin
4 LcSScAnticentromereIatrogenic abdominal bleeding due to ascites punction13ERA, PDE-5 inhibitor
5 LcSScANAPost- LTX130,42Prostacyclin

Abbreviations: ANA: antinucleolar antibody; ERA: endothelin receptor antagonist; LcSSc: Limited cutaneous SSc; LTX: lung transplantation; PDE-5: phosphodiesterase 5; RV: right ventricle; SScPAH: Systemic sclerosis-associated pulmonary arterial hypertension. According to [13]. Since first non-Raynaud symptom, at time of diagnosis of pulmonary arterial hypertension. Ascites caused by RV failure.

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