A Review of Primary Vasculitis Mimickers Based on the Chapel Hill Consensus Classification

Table 3

Comparison of conditions that mimic MVV.

	SAM	FMD	PAN	KD	IE/MA
Age of presentation	40–60	20–30	40–60	0–5	Any
Sex predisposition (F : M)	Equal	3 : 1	Equal	1 : 1.5	Equal
Most frequent anatomical sites	Visceral mesenteric arteries	Renal arteries	Intra-abdominal arteries	Coronary arteries	Any
Radiological features	“String of beads” appearance and dissections with alternating stenosis and aneurysms, thrombosis	Classic “string of beads” appearance with alternating stenosis and aneurysms, rarely dissections	Characteristic microaneurysms predominantly at vessel branch points	Coronary aneurysms in 15–20% of cases	Pseudoaneurysms at branch points
Histologic features	Media predominantly involved with alternating stenoses and aneurysms	All vessel layers may be affected; Pattern depends on histologic subtype	Focal areas of necrotizing panarteritis	Perivasculitis and vasculitis of microvessels with vessel wall edema	Infectious elements present