Review Article
A Review of Primary Vasculitis Mimickers Based on the Chapel Hill Consensus Classification
Table 3
Comparison of conditions that mimic MVV.
| | SAM | FMD | PAN | KD | IE/MA |
| Age of presentation | 40–60 | 20–30 | 40–60 | 0–5 | Any | Sex predisposition (F : M) | Equal | 3 : 1 | Equal | 1 : 1.5 | Equal | Most frequent anatomical sites | Visceral mesenteric arteries | Renal arteries | Intra-abdominal arteries | Coronary arteries | Any | Radiological features | “String of beads” appearance and dissections with alternating stenosis and aneurysms, thrombosis | Classic “string of beads” appearance with alternating stenosis and aneurysms, rarely dissections | Characteristic microaneurysms predominantly at vessel branch points | Coronary aneurysms in 15–20% of cases | Pseudoaneurysms at branch points | Histologic features | Media predominantly involved with alternating stenoses and aneurysms | All vessel layers may be affected Pattern depends on histologic subtype | Focal areas of necrotizing panarteritis | Perivasculitis and vasculitis of microvessels with vessel wall edema | Infectious elements present |
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