BPI-ANCA and Long-Term Prognosis among 46 Adult CF Patients: A Prospective 10-Year Follow-Up Study

Table 1

Characteristics of the adult CF cohort at the time of BPI-ANCA sampling (1995–1998).

Number of patients: (𝑛)
Total	46
Males	26
Females	20
Age: (years)
Mean	26.2
Range	18.4–44.6
CFTR mutation: (𝑛)
ΔF508del/ΔF508del	24
Others	22
FEV1.0 % predicted: (𝑛)
>80%	16
50–80%	17
<50%	13
IgA BPI-ANCA:
Negative (≤67 U)
(𝑛)	17
(mean age, years)	27.5
Positive (>67–200 U)
(𝑛)	18
(mean age, years)	26.3
High (>200 U)
(𝑛)	11
(mean age, years)	24.6
Leeds classification of PsA colonization: (𝑛)
I (chronic)	24
II (intermittent)	2
III (free of PsA)	8
IV (never PsA)	12
Diabetes mellitus: (𝑛)
Yes	5
No	34
NA	1