Review Article
Pulmonary Arterial Hypertension in Systemic Lupus Erythematosus: Current Status and Future Direction
Table 2
Pathology of systemic lupus erythematosus associated pulmonary hypertension.
| Pathological changes in arteries, arterioles and veins | |
| (i) Medial hypertrophy | | (ii) Chronic intimal fibrosis | | (iii) Periadventitial fibrosis | | (iv) Alteration of elastic laminae | | (v) Necrotizing fibrinoid arteriopathy | | (vi) Aneurysmal dilatation and plexiform lesions | |
| Pathological changes in Thrombotic Arteriopathy | |
| (i) Intimal eccentric fibrous thickening | | (ii) Luminal occlusion with recanalization | | (iii) Plexiform lesions coexistent with intimal thrombotic lesions in some arteries | | (iv) Concentric laminar intimal fibrosis not present | |
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