Idiopathic Non Cirrhotic Portal Hypertension and Spleno-Portal Axis Abnormalities in Patients with Severe Primary Antibody Deficiencies

Table 1

Demographic, clinical, and laboratory characteristics of 117 PAD patients.

Female (%)	55.6	ALT (mg/dL)	24 ± 12*
Age (years, mean ± SD)	49 ± 15	AST (mg/dL)	23 ± 18*
Follow-up (years, mean ±SD)	18 ± 14	AP (mg/dL)	98 ± 63*
XLA (%)	4.2	Bilirubin (mg/dL)	0.5 ± 0.4*
CVID (%)	95.8	γGT (mg/dL)	28 ± 26*
Splenomegaly (%)	60.7	INR	1 ± 0.08*
Portal vein enlargement (%)	25.6	RBC (cell/mm^3)	4700000 ± 9430*
Esophageal varices (%)	3.4	Hb (g/dL)	13.4 ± 6*
Portal vein collaterals, other than varices (%)	0.8	WBC (cell/mm^3)	6300 ± 2400*
Ascites (number of patients)	0	PLT (cell/mm^3)	214000 ± 93000*
		IgG at diagnosis (mg/dL)	267 ± 175*
		IgA at diagnosis (mg/dL)	27 ± 36*
		IgM at diagnosis (mg/dL)	42 ± 79*

 *All laboratory parameters are expressed as mean ± SD.