Research Article
Idiopathic Non Cirrhotic Portal Hypertension and Spleno-Portal Axis Abnormalities in Patients with Severe Primary Antibody Deficiencies
Table 2
Clinical data of 117 PAD patients: without spleno-portal axis abnormalities and with isolated splenomegaly and spleno-portal axis abnormalities.
| | PAD with normal spleen and portal diameters () | Isolated splenomegaly () | PAD with spleno-portal axis abnormalities () |
| Time of PAD disease (years)* | 14.3 ± 13.8 | 17 ± 16.5 | 19.7 ± 13 | Bronchiectasis | 15 (33%) | 13 (32%) | 21 (70%) | Gastroenteritis | 15 (33%) | 13 (32%) | 28 (93%) | Lymphoid nodular hyperplasia | 4 (9%) | 2 (5%) | 15 (50%) | Pneumonia | 28 (61%) | 10 (24%) | 19 (63%) | Autoimmunity | 13 (28%) | 6 (15%) | 11 (37%) | Portal vein diameter (mm)* | 10.3 ± 1.7 | 11 ± 1.5 | 14 ± 3 | Spleen diameter (cm)* | 10 ± 1 | 13 ± 2.7 | 14.1 ± 6.3 |
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*Parameters are expressed as mean ± SD.
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