Research Article

Idiopathic Non Cirrhotic Portal Hypertension and Spleno-Portal Axis Abnormalities in Patients with Severe Primary Antibody Deficiencies

Table 2

Clinical data of 117 PAD patients: without spleno-portal axis abnormalities and with isolated splenomegaly and spleno-portal axis abnormalities.

PAD with normal spleen and portal diameters
( )
Isolated splenomegaly
( )
PAD with spleno-portal axis abnormalities
( )

Time of PAD disease (years)*14.3 ± 13.817 ± 16.519.7 ± 13
Bronchiectasis 15 (33%)13 (32%)21 (70%)
Gastroenteritis15 (33%)13 (32%)28 (93%)
Lymphoid nodular hyperplasia4 (9%)2 (5%)15 (50%)
Pneumonia28 (61%)10 (24%)19 (63%)
Autoimmunity13 (28%)6 (15%)11 (37%)
Portal vein diameter (mm)*10.3 ± 1.711 ± 1.514 ± 3
Spleen diameter (cm)*10 ± 113 ± 2.714.1 ± 6.3

 *Parameters are expressed as mean ± SD.