BPI-ANCA Provides Additional Clinical Information to Anti-Pseudomonas Serology: Results from a Cohort of 117 Swedish Cystic Fibrosis Patients

Table 1

Description of the cohort at enrolment.

	Chronic PsA; Leeds 1	Intermittent PsA; Leeds 2	Free from PsA; Leeds 3	Never had PsA; Leeds 4	Total
n	48	11	16	42	117
Median age (IQR) years	21; (17–27)	17; (10–23)	15; (7–22)	16; (7–25)	19; (11–25)
Sex m/f	27/21	4/7	5/10	24/18	60/57
Mutation; ΔF508/ΔF508; ΔF508/other; Other/other; ΔF508/unknown	28/17/2/1	7/4/0/0	10/5/1/0	20/16/3/3	65/42/6/4
Pancreatic insufficiency (%)	47 (98%)	8 (73%)	14 (87,5%)	31 (74%)	100 (85%)
Median lung function (IQR) FEV% pred.	62%; (41–85)	95%; (90–101)	90%; (74–102)	89%; (80–104)	(); 84% (60–96)